Objectives: Ectrodactyly-ectodermal dysplasia-clefting syndrome (EEC) is a rare syndrome with features of ectrodactyly, ectodermal dysplasia and cleft lip/palate. This study presents an Iranian case with classic features and oral complications.Case: We report a 20-year old female with all manifestations of this syndrome. The simultaneous presence of these three malformations is extremely rare; the incidence is estimated to be 1.5 per 100.000.000 births.Conclusion: Oral hygiene management of patients with EEC syndrome is important and dental practitioners need to know the oral and dental conditions presenting with this syndrome.

Dysplasia epiphysealis hemimelica is extremely rare condition. Asymmetrical abnormal cartilage proliferation and associated enchondral ossification in an epiphysis is characteristic. It is limited to the medial or laeral half of a single limb. A child with dysplasia epiphysealis hemimelica of the knee is reported.

Background & Aim: Regional odonto dysplasia (ROD) is an unusual nonhereditary of teeth with significantly clinical and radiographic features. Affected teeth usually remain unerupted or semi-erupted with a discoloration and irregular shape. Radiographically these teeth have a large pulp chamber and thin layer of enamel and dentin with similar density.This article is introducing a female patient who was affected by regional odonto dysplasia (ROD) (a developmental abnormality) and treatment of this patient.Case Report: This patient is a ten-year-old girl was referred to us with unerupted anterior maxillary teeth. Her parents stated that the CBA l  A teeth were extracted at the age of 3 for infection. At the first appointment the erupted left maxillary central tooth had malformation, discoloration and a related fistula with infected drainage. The 321l  teeth germs were not erupted. Due to surgical procedure the left permanent incisor (IV was extracted and right permanent central, lateral and canine (321l ) were enucleated, and appropriate prosthetic treatment was performed for patient after a while.

The concomitance of hypophosphatemic Osteomalacia and polyostotic Fibrous Dysplasia has only been reported to date in a few cases in literature.We have not found any case in medline search in last 7 years. A 22 years old male was admited to the endocrine department because of bone pain. In physical examination typical pigmented cafe-au-Iait lesion of the skin with irregular border was noted only in the left side.Numerous bone cystsand Shepherd's crook deformity of the femur in the radiography and leonine appearance confirmed the diagnosis of polyostotic Fibrous Dysplasia.Persistent low serum phosphate and high urinary excretion of phosphate (in 24 her urine) confirmed concomitanee of hypophosphatenie Osteomalacia.Patients symptoms improved markedly after treatment with calcitriol (Rocaltrol) and phosphate.

Objectives Dentin dysplasia (DD) is a rare disorder, which is not accentuated in dental practice. DD has 2 types. Type I is manifested by tooth mobility, short roots, reduced pulp space and normal crowns. Type II or coronal DD is characterized by normal crowns in permanent teeth but discolored crowns in primary teeth. Denticles are detectable in the pulp chamber of teeth in type II DD. Many uncertain aspects of this condition include its etiology, diagnosis, and treatment planning. For a long time, extraction of mobile teeth was the main possible choice, which would lead to psychosocial problems that needed psychological interventions. The present study aimed to collect and classify the recent information on DD. Methods An electronic search of the literature was carried out in PubMed and Google Scholar from 1977 to 2018. Duplicates were eliminated and the retrieved articles and relevant textbooks were thoroughly reviewed. Results Although DD has an unknown etiology, it is known for a fact that it has a hereditary trait. The present article provides some information about DD, including possible etiological factors, clinical, radiographic and histological manifestations, diagnosis and current treatment options. Conclusion Management of DD is based on preservation of teeth in the oral cavity and may vary from preventive and piecemeal care to tooth extraction and regenerative pulp therapy.