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Information Journal Paper

Title

KINDLER SYNDROME: 2 CASE REPORTS FROM INDIA

Author(s)

 SALODKAR A. | CHOUDHARY S. | KOLEY S.

Pages

  51-54

Abstract

 Kindler syndrome (KS) is a rare autosomal recessive genodermatosis. We report two cases of KS with classical clinical presentations involving skin and mucus membranes. Clinically, both patients had four major features of KS in the form of ACRAL SKIN BLISTERING, PHOTOSENSITIVITY, progressive POIKILODERMA, and diffuse CUTANEOUS ATROPHY. Case 1 had associated features in the form of urethral stenosis, skin fragility and palmoplantar keratoderma with extension of the scaling onto the flexor aspect of the wrist and loss of palmar creases. Case 2 had associated features in form of anal stenosis, oesophageal stenosis, skin fragility and palmoplantar keratoderma with loss of palmar creases. An Interesting finding in our report is that both cases have prominent telengectasia involving face and neck regions.

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    APA: Copy

    SALODKAR, A., CHOUDHARY, S., & KOLEY, S.. (2009). KINDLER SYNDROME: 2 CASE REPORTS FROM INDIA. IRANIAN JOURNAL OF DERMATOLOGY, 12(3 (49 SUPPLEMENT)), 51-54. SID. https://sid.ir/paper/567766/en

    Vancouver: Copy

    SALODKAR A., CHOUDHARY S., KOLEY S.. KINDLER SYNDROME: 2 CASE REPORTS FROM INDIA. IRANIAN JOURNAL OF DERMATOLOGY[Internet]. 2009;12(3 (49 SUPPLEMENT)):51-54. Available from: https://sid.ir/paper/567766/en

    IEEE: Copy

    A. SALODKAR, S. CHOUDHARY, and S. KOLEY, “KINDLER SYNDROME: 2 CASE REPORTS FROM INDIA,” IRANIAN JOURNAL OF DERMATOLOGY, vol. 12, no. 3 (49 SUPPLEMENT), pp. 51–54, 2009, [Online]. Available: https://sid.ir/paper/567766/en

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