Paper Information

Journal:   IRANIAN JOURNAL OF DERMATOLOGY   Fall 2004 , Volume 8 , Number Supplement 1; Page(s) 39 To 46.
 
Paper: 

PRETIBIAL EPIDERMOLYSIS BULLOSA: REPORT OF TWO CASES

 
 
Author(s):  YAGHOUBI R., SINA N., EMAD MOSTOJI N., RAJIEI R.
 
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Abstract: 
Pretibial epidermolysis bullosa is a rare variant of hereditary epidermolysis bullosa characterized by the delayed onset of lesions andtheir localization. We present two cases, a 35-year-old woman and a 21-year-old man. They clinically had pruritus, nodular prurigo- like or lichenified lesions, violaceous scarring, milia, nail dystrophy and iil one case albopapuloid lesions on the trunk. Physical signs of disease were first noticed between 3 and 9 years of age. . Histologic examination showed a subepidermal blister with milia formation, and a mild mixed inflammatory ,infiltrate. These patients represent an unusual, poorly recongnized form of dystrophic epidermolysis bullosa with features that resemble a variety of acquired dermatoses.
 
Keyword(s): DYSTROPHIC EPIDERMOLYSIS BULLOSA, PRETIBIAL, ALBOPAPULOID LESIONS, ANCHORING FIBRILS
 
References: 
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