Paper Information

Journal:   ACTA MEDICA IRANICA   JANUARY-FEBRUARY 2008 , Volume 46 , Number 1; Page(s) 84 To 86.
 
Paper: 

CONGENITAL SELF HEALING CUTANEOUS LANGERHANS CELL HISTIOCYTOSIS WITH MULTIPLE HYPOPIGMENTED MACULES AFTER RECOVERY IN A NEONATE

 
 
Author(s):  RAMYAR A., YAGHMAEI B.*, MONAJEMZADEH M.
 
* DEPARTMENT OF PEDIATRIC, CHILDREN'S HOSPITAL MEDICAL CENTER, SCHOOL OF MEDICINE, MEDICAL SCIENCES, UNIVERSITY OF TEHRAN, TEHRAN, IRAN
 
Abstract: 

Langerhans cell histiocytosis (LCH) is the most common type of childhood histiocytic disorder with an incidence of 0.2 to 1 per 100,000 children under the age of 15 years (1). The clinical picture of LCH varies from single system (S-S)bone or skin disease to multi-system disease (M-S) (2). We report a neonate with disseminated papulonodular eruption containing mononuclear CD1a and S100 positive histiocytic cells infiltration at epidermis and underlying dermis. The diagnosis of a congenital self healing Langerhans cell histiocytosis (CSHLCH) was made and follow up showed a complete recovery of the eruptions , leaving hypopigmented macules in the sites corresponding to the initial findings.

 
Keyword(s): CONGENITAL SELF HEALING LANGERHANS CELL HISTIOCYTOSIS (CSHLCH), LANGERHANS CELL HISTIOCYTOSIS (LCH), HASHIMATO PRITZKER DISEASE
 
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